l carnitine function transports long chain fatty acids into mitochondria Carnitine: Genetic Variants Affecting Mitochondrial Energy and Health The carnitine shuttle system. Carnitine
Description
They may do this by increasing the amount eliminated in urine

(2000) found no effect of 2 g/day L-carnitine for 8 weeks in obese women [7][62]

10.3389/fimmu.2021.677879 146 SternA

High-functioning mitochondria support: Consistent physical energy Metabolic flexibility (using both fats and carbs for fuel) Cognitive performance Recovery from activity ALCs Role in Energy Production Acetyl-L-Carnitines primary job is to shuttle fatty acids into the mitochondria so they can be burned for fuel
While it is found in meat and dairy and produced by the body, supplementation may offer benefits for weight management, brain function, heart health, and blood sugar control

The clinical abnormalities observed vary for each specific UCD, but most patients tend to have similar symptoms 14