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It had previously been shown that the amino acid sequence DEETGE is essential for NRF2-KEAP1 interaction [124]

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Remarkably, a single mutation in the ND4 subunit of complex I is adequate to trigger LHON, as elucidated in a study on mice

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For instance, in the aforementioned study of Herrmann et al

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Nature 420 , 806 (2002)

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